CASE REPORT |
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Year : 2014 | Volume
: 6
| Issue : 2 | Page : 71-74 |
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Parry-Romberg syndrome: A linear variant of scleroderma with discoid lupus erythematosus on scalp - an association
Pragya A Nair, Nidhi H Patel, Nilofar G Diwan
Department of Dermatology and Venereology, Pramukshwami Medical College, Karamsad, Gujarat, India
Correspondence Address:
Pragya A Nair Department of Dermatology and Venereology, Pramukhswami Medical College, Karamsad - 388 325, Gujarat India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/0974-7753.138594
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Parry-Romberg syndrome is a rare neurocutaneous syndrome characterized by progressive shrinkage and degeneration of the tissues beneath the skin, usually on one side of the face. It is associated with neurological disorders such as trigeminal neuralgia, facial paresthesia, headache, and focal epilepsy. Concomitant occurrence of discoid lupus erythematosus (DLE) and morphea in the same skin lesion is exceptional, defined as overlap syndrome with two or more different connective tissue disease concurrently or consecutively. A 32-year-old female developed DLE on a long-standing lesion of scleroderma over left temporal area with characteristics histopathological changes. She was treated with oral antimalarials and steroids which halted the progress of the disease. |
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